Case Reports and Reviews: Open Access

Abstract 

Introduction: Darier-Ferrand dermatofibrosarcoma (DFS) is a rare cutaneous mesenchymal tumour, the extent of tumour spread of which is often underestimated. It is distinguished by its local aggressiveness and its significant potential for recurrences, the prognosis of which is contingent on the quality of the patient's care. The management of localized forms is based on broad surgery, with meticulous evaluation of the margins. Treatment is based on surgery. Objective: To describe the management of frontal Darier-Ferrand dermatofibrosarcoma. Observation: This is a 23-year-old patient, with no medical or surgical history, who had consulted the Department of Stomatology and Maxillofacial Surgery of the CHUO for frontal swelling that had been evolving for two months. The clinical examination revealed a swelling resting on an indurated surface. A biopsy was performed under local anaesthesia, and the anatomo-pathological result was a Darier-Ferrand dermatofibrosarcoma. Subsequent to this, a broad excision with substance loss coverage (PDS) from a thin skin graft on the inner side of the thigh was performed. Conclusion: Dermato fibrosarcoma is a skin tumor whose frontal location is unusual and very rare. Surgery with significant margins for resection in healthy areas, covering the loss of substance by skin grafting is the solution.
 

Keywords: Surgical treatment, Dermarofibrosarcoma, Recurrence.